Mesenteric fibromatosis involving intestine mimicking a gastrointestinal stromal tumor

Sakshi J. Parmar; Manmohan M. Kamat; Avani Mishra; Saisree Setipalli

doi:10.18203/2349-2902.isj20231976

Authors

Sakshi J. Parmar Department of General Surgery, Nanavati Max Super Speciality Hospital, Mumbai, Maharashtra, India https://orcid.org/0009-0003-3235-4575
Manmohan M. Kamat Department of General Surgery, Nanavati Max Super Speciality Hospital, Mumbai, Maharashtra, India
Avani Mishra Department of General Surgery, Nanavati Max Super Speciality Hospital, Mumbai, Maharashtra, India
Saisree Setipalli Department of General Surgery, Nanavati Max Super Speciality Hospital, Mumbai, Maharashtra, India

DOI:

https://doi.org/10.18203/2349-2902.isj20231976

Keywords:

Mesenteric fibromatosis, Intestinal involvement, GIST, Desmoid tumour

Abstract

Mesenteric fibromatosis (MF) or intra-abdominal desmoid tumour is a rare proliferative disease affecting the mesentery. MF is a locally aggressive tumour that lacks metastatic potential, but the local recurrence is common. We report a case of 33-year-old female with chief complaints of mass in abdomen which was hard on palpation arising from the pelvis and extending up to the umbilicus. Magnetic resonance imaging (MRI) suggestive of soft tissue mass and exploration was planned. Intra-operatively a mass of 16×16×8 cm with attached ileum and caecum which was excised completely and sent for histopathological examination. Histopathology was suggestive of Mesenteric fibromatosis spindle cell type. Considering the rarity of this tumour and difficulties in diagnostic and therapeutic ambit, we believe it is justified to publish this case which came to our observation.

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References

Stanford School of Medicine. Surgical Pathology Criteria. 2005. Available at: https://surgpath criteria.stanford.edu/softfib/mesenteric_fibromatosis/printable.htm. Accessed on 12 February 2023.

Destri GL, Ferraro MJ, Calabrini M, Pennisi M, Magro G. Desmoid-type fibromatosis of mesentery. Case Rep Med. 2014;850180.

Haibin J, Wentao Z, Baolei Z, Jian S, Qiang W, Baofang S, et al. A giant mesenteric fibromatosis involving the muscular layer of the colon wall: A case report. Medicine. 2019;98(1):e14015.

Dalén BP, Geijer M, Kvist H, Bergh PM, Gunterberg BU. Clinical and imaging observations of desmoid tumors left without treatment. Acta Orthop. 2006;77(6):932-7.

Nicolas G, Kfoury T, Shimlati R, Tohme M, Wakim R. Incidental Finding and Management of Mesenteric Fibromatosis. Am J Case Rep. 2016;17:389-94.