Dermatofibrosarcoma protuberans of perianal region: a rare case report
DOI:
https://doi.org/10.18203/2349-2902.isj20221428Keywords:
DFSP, Abdominoperineal, Soft tissue sarcomaAbstract
Dermatofibrosarcoma protuberans (DFSP) is a rare locally aggressive slow growing soft tissue sarcoma with very low metastatic potential with high local recurrence rates. We presented a rare case of DFSP of left perianal region ulcerating into anal canal, we did wide excision with 3 cm margin along with abdominoperineal excision of rectum and permanent colostomy, defect is reconstructed with left pedicled antero-lateral thigh flap. DFSP has high chance of recurrence, it should be excised with at least 2-3 cm 3D margin and patient should be followed up for a long time.
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