DOI: http://dx.doi.org/10.18203/2349-2902.isj20221428

Dermatofibrosarcoma protuberans of perianal region: a rare case report

Subbiah Shanmugam, Radha Siva Bharath

Abstract


Dermatofibrosarcoma protuberans (DFSP) is a rare locally aggressive slow growing soft tissue sarcoma with very low metastatic potential with high local recurrence rates. We presented a rare case of DFSP of left perianal region ulcerating into anal canal, we did wide excision with 3 cm margin along with abdominoperineal excision of rectum and permanent colostomy, defect is reconstructed with left pedicled antero-lateral thigh flap. DFSP has high chance of recurrence, it should be excised with at least 2-3 cm 3D margin and patient should be followed up for a long time.


Keywords


DFSP, Abdominoperineal, Soft tissue sarcoma

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References


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