A rare case of adult Wilms tumor: case report and literature review from a tertiary centre

Authors

  • Sameer Trivedi Department of Urology, Institute of Medical Science, Sir Sunder Lal Hospital, BHU, Varanasi, Uttar Pradesh, India
  • K. Shridhar Reddy Department of Urology, Institute of Medical Science, Sir Sunder Lal Hospital, BHU, Varanasi, Uttar Pradesh, India
  • Mahima Yadav Department of Pathology, Institute of Medical Science, Sir Sunder Lal Hospital, BHU, Varanasi, Uttar Pradesh, India
  • Lalit Kumar Agrawal Department of Pathology, Institute of Medical Science, Sir Sunder Lal Hospital, BHU, Varanasi, Uttar Pradesh, India
  • Ujwal Kumar Department of Pathology, Institute of Medical Science, Sir Sunder Lal Hospital, BHU, Varanasi, Uttar Pradesh, India
  • Yashasvi Singh Department of Pathology, Institute of Medical Science, Sir Sunder Lal Hospital, BHU, Varanasi, Uttar Pradesh, India

DOI:

https://doi.org/10.18203/2349-2902.isj20214019

Keywords:

Nephroblastoma, Adult Wilms’ tumor, Renal tumor

Abstract

Nephroblastoma (Wilms’ tumour) in adult population is extremely rarefied scenario and has a poorer prognosis than paediatric Wilms’ tumour with an incidence of about 0.2 per million per year in the USA and Europe. Clinical presentation is also distinct between children and adults. In adults, manifestation is usually hematuria and abdominal pain while paediatric cases frequently present with an asymptomatic abdominal lump. It is arduous to demarcate adult Wilms’ tumour from renal cell carcinoma based on radiology alone. The final diagnosis in adult cases is often fortuitous following radical nephrectomy for presumed adult Renal cell carcinoma (RCC). Due to the lack of published discussion, there are no standard protocols for the management of adult Wilms tumour (WT) hence it is managed as per paediatric WT. In view of this, we report a case of adult WT in a 32-years-old female, who was diagnosed propitiously following right radical nephrectomy for an assumed right renal mass.  

Author Biographies

Sameer Trivedi, Department of Urology, Institute of Medical Science, Sir Sunder Lal Hospital, BHU, Varanasi, Uttar Pradesh, India

Professor & Head, Department of Urology, Institute of Medical Science, BHU, Varanasi, 221005, U.P, India

K. Shridhar Reddy, Department of Urology, Institute of Medical Science, Sir Sunder Lal Hospital, BHU, Varanasi, Uttar Pradesh, India

M.Ch Trainee, Department of Urology, Institute of Medical Science, BHU, Varanasi, 221005, U.P, India

Mahima Yadav, Department of Pathology, Institute of Medical Science, Sir Sunder Lal Hospital, BHU, Varanasi, Uttar Pradesh, India

Assistant Professor, Department of Pathology, Institute of Medical Science, BHU, Varanasi, 221005, U.P, India

Lalit Kumar Agrawal, Department of Pathology, Institute of Medical Science, Sir Sunder Lal Hospital, BHU, Varanasi, Uttar Pradesh, India

Assistant Professor, Department of Urology, Institute of Medical Science, BHU, Varanasi, 221005, U.P, India

Ujwal Kumar, Department of Pathology, Institute of Medical Science, Sir Sunder Lal Hospital, BHU, Varanasi, Uttar Pradesh, India

Assistant Professor, Department of Urology, Institute of Medical Science, BHU, Varanasi, 221005, U.P, India

Yashasvi Singh, Department of Pathology, Institute of Medical Science, Sir Sunder Lal Hospital, BHU, Varanasi, Uttar Pradesh, India

Assistant Professor, Department of Urology, Institute of Medical Science, BHU, Varanasi, 221005, U.P, India

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Published

2021-09-28

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Section

Case Reports