Primary fibrosarcoma of breast: a rare case presentation
DOI:
https://doi.org/10.18203/2349-2902.isj20151113Keywords:
Fibrosarcoma, FNAC, Incisional biopsy, Modified radical mastectomyAbstract
Primary Fibrosarcoma of breast is an extremely rare tumor accounting for <1% of all the primary breast malignancies and <5% of all the sarcomas. Breast fibrosarcoma is a rare tumor characterized by marked rapidity of growth. Diagnostic investigations like FNAC, mammography and USG are relatively insensitive and histopathological diagnosis is mainstay and it is usually a diagnosis of exclusion. Surgical therapy is most effective treatment and chemotherapy should be considered for large tumors with high mitotic rates. In all the diagnosis and management should be multidisciplinary team approach. In this case report we are reviewing a case of primary Fibrosarcoma of breast in a 45 years old female presenting with a rapidly growing painless mass in left breast since 3 months. Repeated FNAC were inconclusive and hence incisional biopsy was done which revealed Fibrosarcoma. Modified radical mastectomy was done with axillary clearance and histopathology reports further confirmed the diagnosis. Being a very rare tumor, the primary aim of this presentation is to provide an overview of literature on the diagnosis and management protocols for breast fibrosarcoma patients.
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