Acute intestinal obstruction in Peutz Jeghers syndrome: a case report

Authors

  • Gajendra Anuragi Department of Surgical Gastroenterology, Madras Medical College, Chennai, Tamil Nadu, India
  • Afroz I. Bagwan Department of Surgical Gastroenterology, Madras Medical College, Chennai, Tamil Nadu, India
  • Ramprakash V. S. Department of Surgical Gastroenterology, Madras Medical College, Chennai, Tamil Nadu, India
  • Sugumar C. Department of Surgical Gastroenterology, Madras Medical College, Chennai, Tamil Nadu, India
  • Naganath B. O. Lakshmanamoorthy Department of Surgical Gastroenterology, Madras Medical College, Chennai, Tamil Nadu, India

DOI:

https://doi.org/10.18203/2349-2902.isj20214017

Keywords:

Peutz Jeghers syndrome, Autosomal dominant, Malignancy, Intussusception

Abstract

Peutz Jeghers syndrome is an autosomal dominant hereditary disorder affecting male and female equally. It is characterised by mucocutaneous hyperpigmentation and hamartomatous polyp in gastrointestinal tract with increased risk of malignancy. We report here a case of 52-year-old patient with traits of Peutz jeghers syndrome presented with acute intestinal obstruction following colocolic intussusception. Peutz jeghers syndrome is an autosomal dominant inherited disorder. Individual may present in rare case with acute intestinal obstruction associated with intussusception due to polyps.

References

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Published

2021-09-28

Issue

Section

Case Reports