Bowel perforation in Dego’s disease: a lethal surgical scenario
DOI:
https://doi.org/10.18203/2349-2902.isj20151489Keywords:
Kohlmeier, Dego’s disease, Manifestation, TreatmentAbstract
Malignant atrophic papulosis or Dego’s disease is a type of cutaneous disease with involvement of the gastrointestinal and central nervous system. Involvement of the gastrointestinal system by way of perforation invariably leads to a fatal outcome. Awareness of this condition will help in providing a high index of suspicion while managing unexplained multiple intestinal perforations or while dealing with rapidly developing complications in perforative peritonitis.
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