DOI: http://dx.doi.org/10.18203/2349-2902.isj20205393

Laparoscopic correction of midgut volvulus due to malrotation in a patient with Marfans syndrome

Saurabh Sharma, Radha Govind Khandelwal, Prabha Om

Abstract


This case describes 13-year-old female with Marfans syndrome who presented recurrent small intestinal obstruction which was later diagnosed as acute midgut volvulus due to malrotation after extensive workup. Laparoscopic Ladd’s procedure was performed. Patient had uneventful recovery and discharged on post-operative day five. To best of our knowledge the index case is the first case of laparoscopic ladds procedure in known case of Marfans syndrome.


Keywords


Marfans syndrome, Laparoscopic Ladd’s procedure, Intestinal malrotation, Midgut volvulus

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References


Kasper DL, Fauci AS, Hauser SL, Longo DL, Jameson JL, Loscalzo J. Harrison's Principles of Internal Medicine. 2015;19:2512-13.

Papadimitriou G, Marinis A, Papakonstantinou A. Primary midgut volvulus in adults: report of two cases and review of the literature. J Gastrointest Surg. 2011;15:1889-92.

Welch GH, F.R.C.S, Anderson JR. Volvulus of the Small Intestine in Adults. World J. Surg. 101986:496-500.

Inayet N. Gastrointestinal Manifestations of Marfan Syndrome. 2017;10.20944.

Vaez-Zadeh K, Dutz W, Nowrooz-Zadeh M. Volvulus of the small intestine in adults: a study of predisposing factors. Ann Surg. 1969;169:265-71.

Robinson PN, Arteaga-Solis E, Baldock C, Collod-Béroud G, Booms P, De Paepe A, et al. The molecular genetics of Marfan syndrome and related disorders. J Med Genet. 2006;43:769-87.

Junpaparp P, Chayanupatkul M, Buppajarntham S, Phowthongkum P. Sigmoid volvulus: is it related to marfan syndrome? Int J Colorectal Dis. 2014;29:771-2.

Guragain R, Zeinab A, Cheng M, Karki P, JB. Primary midgut volvulus in a patient with Marfan syndrome. J Surg Case Rep. 2019;2019(2):31.

van der Zee DC, Bax NM. Laparoscopic repair of acute volvulus in a neonate with malrotation. Surg Endosc. 1995;9:1123-4.

Youssef MA. Laparoscopic Ladds procedure in infants: Report of three cases from a developing country. J Minim Access Surg. 2008;4:83-4.

Isani MA, Schlieve C, Jackson J, Elizee M, Asuelime G, Rosenberg D et al. Is less more? Laparoscopic versus open Ladd’s procedure in children with malrotation. Journal of surgical research. 2018;229:351-56.

Nakajima Y, Sakata H, Yamaguchi T, Yoshie N, Yamada T, Osako T et al. Successful treatment of a 14-year-old patient with intestinal malrotation with laparoscopic Ladd procedure: case report and literature review. World Journal of Emergency Surgery. 2013;8:19.

Reddy AS, Shah RS, Kulkarni DR. Laparoscopic ladd's procedure in children: challenges, results, and problems. J Indian Assoc Pediatr Surg. 2018;23:61-5.

Butterworth WA, Butterworth JW. An adult presentation of midgut volvulus secondary to intestinal malrotation: A case report and literature review. Int J Surg Case Rep. 2018;50:46-9.