Laparoscopic correction of midgut volvulus due to malrotation in a patient with Marfans syndrome

Authors

  • Saurabh Sharma Department of General Surgery, SMS Hospital and Medical College, Jaipur, Rajasthan, India http://orcid.org/0000-0002-8883-1946
  • Radha Govind Khandelwal Department of General Surgery, SMS Hospital and Medical College, Jaipur, Rajasthan, India
  • Prabha Om Department of General Surgery, SMS Hospital and Medical College, Jaipur, Rajasthan, India

DOI:

https://doi.org/10.18203/2349-2902.isj20205393

Keywords:

Marfans syndrome, Laparoscopic Ladd’s procedure, Intestinal malrotation, Midgut volvulus

Abstract

This case describes 13-year-old female with Marfans syndrome who presented recurrent small intestinal obstruction which was later diagnosed as acute midgut volvulus due to malrotation after extensive workup. Laparoscopic Ladd’s procedure was performed. Patient had uneventful recovery and discharged on post-operative day five. To best of our knowledge the index case is the first case of laparoscopic ladds procedure in known case of Marfans syndrome.

Author Biographies

Saurabh Sharma, Department of General Surgery, SMS Hospital and Medical College, Jaipur, Rajasthan, India

MBBS, MS (JR3) DEPARTMENT OF GENERAL SURGERY

Radha Govind Khandelwal, Department of General Surgery, SMS Hospital and Medical College, Jaipur, Rajasthan, India

DEPARTMENT OF GENERAL SURGERY

Prabha Om, Department of General Surgery, SMS Hospital and Medical College, Jaipur, Rajasthan, India

DEPARTMENT OF GENERAL SURGERY

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Published

2020-11-27

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Section

Case Reports