A rare large anterior abdominal wall dermatofibrosarcoma protuberans treated by wide local excision and abdominoplasty: a case report and review of the literature

Bader H. Shirah; Hamza A. Shirah; Abubaker E. Elnour; Ayman O. Alsabouni; Mohammad A. Chughtai; Amar H. Hussain

doi:10.18203/2349-2902.isj20150520

Authors

Bader H. Shirah King Abdullah International Medical Research Center / King Saud bin AbdulAziz University for Health Sciences, Jeddah
Hamza A. Shirah Department of General Surgery, Al Ansar General Hospital, Medina
Abubaker E. Elnour Department of General Surgery, Al Ansar General Hospital, Medina
Ayman O. Alsabouni Department of General Surgery, Al Ansar General Hospital, Medina
Mohammad A. Chughtai Department of Radiology, Al Ansar General Hospital, Medina
Amar H. Hussain Department of Pathology, King Fahad General Hospital, Medina

DOI:

https://doi.org/10.18203/2349-2902.isj20150520

Keywords:

Dermatofibrosarcoma protuberans, Spindle cell neoplasm, Abdominoplasty

Abstract

Dermatofibrosarcoma protuberans is a rare soft tissue neoplasm characterized by uniform, slender, spindle shaped, fibroblast like cells, arranged in a typical storiform or cartwheel pattern. Diagnosis is established after excisional biopsy or punch biopsy, CT scan and MRI are useful in both diagnosis and planning the magnitude of wide, free margins surgical excision. Large anterior abdominal wall DFSP represents a challenging modality in reconstructive options. In our paper, we introduce the technique of spindle shaped wide local surgical excision followed by abdominoplasty for a rare large 15×7×4.5 cm, anterior, middle abdominal wall dermatofibrosarcoma protuberans (in the umbilical region). In spite of the large tumor size, and the rare location, the technique is simple, easy to plan and perform, safe for free surgical margins resection, with good cosmetic results, and excellent post operative recovery.

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