DOI: http://dx.doi.org/10.18203/2349-2902.isj20202865

Dermatofibrosarcoma protuberance: a recrudescent dermal malignancy

Nida Khan, Abhishek Mahadik, Manish Kumar, Rubina Hitawala, Khyati Patel

Abstract


Dermatofibrosarcoma protruberens is a rare soft tissue tumour of low malignant potential, commonly seen on the trunk and extremities. It is a slow growing sarcoma, with a tendency for recurrence. Rarely, it may be a high-grade tumour. It responds well to wide local excision. Radiotherapy is beneficial for margin positive and high-grade tumours. We present a case of a 22 years old male with a dermatofibrosarcoma protruberens presenting as a swelling over the left inguinal region since, 4 years, that was excised with a 2cm margin. Patient was followed up for six months without any recurrence.


Keywords


Dermatofibrosarcoma protruberens, Sarcoma, Wide local excision, Imatinib, Spindle cells, Storiform pattern

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References


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