Unusual trichobezor of stomach and intestines as a manifestation of Rapunzel syndrome: a rare case report

Authors

  • Tejinder Pal Singh Sodhi Department of General Surgery, Maharishi Markandeshwar (Deemed to be) University, Mullana, Ambala, Haryana, Punjab, India
  • Sameer Pundeer Department of General Surgery, Maharishi Markandeshwar (Deemed to be) University, Mullana, Ambala, Haryana, Punjab, India
  • Maneshwar Singh Utaal Department of General Surgery, Maharishi Markandeshwar (Deemed to be) University, Mullana, Ambala, Haryana, Punjab, India
  • Kirti Savyasacchi Goyal Department of General Surgery, Maharishi Markandeshwar (Deemed to be) University, Mullana, Ambala, Haryana, Punjab, India

DOI:

https://doi.org/10.18203/2349-2902.isj20195435

Keywords:

Rapunzel syndrome, Trichobezoar, Duodenojejunal junction

Abstract

Rapunzel syndrome is a rare form of trichobezoar with accumulation of large amounts of hair extending from stomach to variable portion of small intestine. An 18 year old girl was brought to surgery opd with complaints of vomiting on and off since 3 months. Contrast enhanced computed tomography abdomen showed a bezoar extending from stomach into the duodenum and proximal jejunum suggestive of Rapunzel syndrome with 3rd and 4th part of duodenum along with duodenojejunal junction. On laparotomy, a trichobezoar occupying the entire stomach measured 100 cm in length and 700 grams in weight. Since the mass formed in Rapunzel syndrome is generally too large to be removed endoscopically or laparoscopically, it requires removal by open gastrostomy. 

References

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Published

2019-11-26

Issue

Vol. 6 No. 12 (2019): December 2019

Section

Case Reports