Median cleft lip: an uncommon and unique anomaly

Authors

DOI:

https://doi.org/10.18203/2349-2902.isj20193369

Keywords:

Median cleft lip, DeMyer sequence, Median cleft face syndrome

Abstract

Median or midline cleft lip [MCL] is an uncommon anomaly characterized by a midline vertical cleft through the upper lip and are either isolated or part of multiple anomalies. It can involve the pre-maxilla, the nasal septum, and the central nervous system. MCL includes Complete (42%), Incomplete (49%), and Minor forms (9%). The three main groups distinguished were: 1. Isolated MCL; 2. MCL with craniofacial malformations; and 3. MCL with extra-facial malformations. To analyze two operated cases of median cleft lip and review the relevant literature. The details of two cases of median cleft lip that were operated in 2017 were analysed. Both cases underwent wedge excision with the classical inverted V incision and muscle reconstruction with satisfactory result. Both the patients had no syndromic association or associated anomaly. All cases of MCL require evaluation for associated abnormalities. Isolated MCL can be repaired surgically with a good outcome. 

References

DeMyer W. The median cleft face syndrome: differential diagnosis of cranium bifidum occultum, hypertelorism, and median cleft nose, lip, and palate. Neurology. 1967;17:961–71.

de Boutray M, Beziat JL, Yachouh J, Bigorre M, Gleizal A, Captier G. Median cleft of the upper lip: A new classification to guide treatment decisions. J Craniomaxillofac Surg. 2016;44(6):664-71.

Urata MM, Kawamoto HK, Median clefts of the upper lip: a review and surgical management of a minor manifestation. J Craniofacial Surg. 2003;14:749–55.

Apesos J, Anigian GM. Median cleft of the lip: its significance and surgical repair. Cleft Palate Craniofacial J. 1993;30:94–6.

Millard DR. Median cleft lip with hypertelorism. In: Millard DR (ed). Cleft craft: The evolution of its surgery: bilateral and rare deformities. Volume 2. Boston: Little, Brown; 1977: 727–68.

Ichida M, Komuro Y, Yanai A. Consideration of median cleft lip with frenulum labii superior. J Craniofacial Surg. 2009;20:1370–4.

Mazzola RF. Congenital malformations in the frontonasal area: their pathogenesis and classification. Clin Plast Surg. 1976;3:573–609.

Millard DR, Williams S. Median Clefts of the upper lip. Plastic Reconstructive Surg. 1968;42:4–14.

Springer IN, Sprengel M, Terheyden H, Suhr MA, Härle F, Warnke PH. Wedge excision: treatment of choice in minimal median clefts of the upper lip. Plast Reconstr Surg. 2004;114:812–4.

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Published

2019-07-25

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Section

Case Reports