Plexiform neurofibromatosis of left upper arm: a rare case report and review of the literature

Authors

  • Satyajeet Verma Department of Surgery, Mahamaya Rajkiya Allopathic Medical College, Ambedkarnagar, Uttar Pradesh 224227, India
  • Sujeet Rai Department of Anaesthesiology, Mahamaya Rajkiya Allopathic Medical College, Ambedkarnagar, Uttar Pradesh 224227, India
  • Zaheer Ahmad Department of Surgery, Mahamaya Rajkiya Allopathic Medical College, Ambedkarnagar, Uttar Pradesh 224227, India

DOI:

https://doi.org/10.18203/2349-2902.isj20163623

Keywords:

Plexiform Neurofibromatosis, Cfe-au-lait spot

Abstract

Giant plexiform neurofibromatosis is a relatively rare manifestation of Type 1 neurofibromatosis. This condition leads to gross disfiguration along with functional disability. Due to the unpredictable natural history and high vascularity of these lesions, the optimal management is still not well defined. We are presenting a 20 year male of Plexifrom Neurofibromatosis of left upper limb. The aim of this rare case report is also to discuss the management difficulties encountered.

References

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Published

2016-12-10

Issue

Vol. 3 No. 4 (2016): October-December 2016

Section

Case Reports