Giant jejunal leiomyosarcoma: a rare case
DOI:
https://doi.org/10.18203/2349-2902.isj20185051Keywords:
Asymptomatic, Bleeding, Chemotherapy, Immunohistochemistry, NulliparousAbstract
Unlike other gastrointestinal neoplasms, small bowel tumours are often rare. Of this, leimyosarcoma of jejnum is extremely uncommon. Most of these patients are asymptomatic however in few cases may present with acute presentation such as intestinal obstruction, bleeding and perforation. A 35 years old female presented to the hospital with complaints of pain and vomiting. On palpation, an irregular 21x18cms lump with variable consistency and irregular borders which was intraabdominal and intraperitoneal. CECT revealed heterogenous, hypoechoic mass extending from epigastric to hypogastric region with probable diagnosis of mesenchymal tumour (probably GIST/LEIOMYOSARCOMA), however exact site of origin couldn’t be traced. Patient underwent exploratory laprotomy, 25x20cms irregular mass arising from jejunum was resected and sent for histopathological examination. HPE and immunohistochemistry revealed grade 3 leiomyosarcoma.
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