Agenesis of dorsal pancreas causing extra hepatic portal vein obstruction in a patient of symptomatic cholelithiasis: a case report

Vipan Kumar; Niraj Gupta; Mohd Muzammil Ambekar; Neeraj Sharma; Prateek Sood; Vikrant Sharma; Narvir Singh Chauhan; Rajkumar Sharma; Somraj Mahajan

doi:10.18203/2349-2902.isj20182799

Authors

Vipan Kumar Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
Niraj Gupta Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
Mohd Muzammil Ambekar Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
Neeraj Sharma Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
Prateek Sood Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
Vikrant Sharma Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
Narvir Singh Chauhan Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
Rajkumar Sharma Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
Somraj Mahajan Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India

DOI:

https://doi.org/10.18203/2349-2902.isj20182799

Keywords:

ADP, Agenesis of dorsal pancreas, EHPVO

Abstract

Agenesis of dorsal pancreas (ADP) is an extremely rare entity. We report a case of 50 year old lady with complete agenesis of the dorsal pancreas presenting with extra-hepatic portal vein obstruction (EHPVO) with symptomatic gall stone disease. Contrast enhanced computed tomography (CECT) revealed a normal pancreatic head, but pancreatic body and tail were not visualized, pancreatic head was compressing upon the portal vein with marked luminal narrowing and cavernoma formation. Magnetic resonance imaging (MRI) and magnetic resonance cholangio pancreatography (MRCP) findings confirmed the CT findings of ADP.

Metrics

Metrics Loading ...

References

Asas Fukuoka K, Ajiki T, Yamamoto M, Fujiwara H, Onoyama H, Fujita T, Katayama N, Mizuguchi K, Ikuta H, Kuroda Y, Hanioka K. Complete agenesis of the dorsal pancreas. J Hepatobiliary Pancreat Surg 1999; 6: 94-97

Schnedl, W.J., Piswanger-Soelkner, C., Wallner, S.J. et al. Dig Dis Sci (2009) 54: 481. https://doi.org/10.1007/s10620-008-0370-3

Fukuoka K, Ajiki T, Yamamoto M, Fujiwara H, Onoyama H, Fujita T, Katayama N, Mizuguchi K, Ikuta H, Kuroda Y, Hanioka K. Complete agenesis of the dorsal pancreas. J Hepatobiliary Pancreat Surg 1999; 6: 94-97

Voldsgaard P, Kryger-Baggesen N, Lisse I. Agenesis of pancreas. Acta Paediatr 1994; 83: 791-793

Saisho Y, Butler AE, Meier JJ, Monchamp T, Allen-Auerbach M, Rizza RA et al (2007) Pancreas volumes in humans from birth to age one hundred taking into account sex, obesity, and presence of type-2 diabetes. Clin Anat 20:933–942. doi:10.1002/ca.20543.