Rare case of recurrent angiosarcoma of the scalp: a case report and review of literature
Keywords:
Angiosarcoma, Vascular neoplasms, Hemangiosarcoma, SarcomaAbstract
Angiosarcoma is a rare soft tissue tumour and forms less than 1% of all sarcomas. It usually occurs in the head and neck, and lesions in the scalp are seen in elderly people. Clinically, it varies from a small plaque to multifocal nodules and ulcers. The treatment varies with the extent of the disease. Most cases are treated with wide excision with reconstruction. Radiotherapy and chemotherapy is advised in the recurrent or extensive lesions with regional or distant metastasis. Recently, immunomodulation have been tried. Authors present a rare case of a 43-year-old female patient having bleeding scalp nodular lesions with ulcers. There was past history of nodular lesion over same area on scalp 17 years back which was diagnosed as angiosarcoma and was treated. On biopsy ulcerative nodular lesions were diagnosed as angiosarcoma. Wide local excision with craniectomy was done. Reconstruction using a latissimus dorsi flap was done at a second stage. The patient was not given postoperative radiotherapy or chemotherapy. There has been no recurrence for two years of follow-up.
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