Poland’s syndrome: a rare case report

Authors

  • Reshma S. Department of General Surgery, Saveetha Medical College and Hospital, Thandalam, Chennai, Tamil Nadu, India
  • Vijai R. Department of General Surgery, Saveetha Medical College and Hospital, Thandalam, Chennai, Tamil Nadu, India
  • Chakarvarthy N. Department of General Surgery, Saveetha Medical College and Hospital, Thandalam, Chennai, Tamil Nadu, India

DOI:

https://doi.org/10.18203/2349-2902.isj20174530

Keywords:

Hypoplasia, Poland’s syndrome, Pectoralis major

Abstract

Poland’s syndrome is a rare congenital condition. It is classically characterized by absence of unilateral chest wall muscles and sometimes ipsilateral symbrachydactyly (abnormally short and webbed fingers). The condition typically presents with unilateral absence of the sternal or breast bone portion of the pectoralis major muscle which may or may not be associated with the absence of nearby musculoskeletal structures. We report a 25-year-old male patient with typical features of Poland’s syndrome. To the best of our knowledge, this is the first documented case of a patient with Poland’s syndrome reported from Chennai.

References

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Published

2017-09-27

Issue

Section

Case Reports