A rare presentation of intraabdominal desmoid tumour
DOI:
https://doi.org/10.18203/2349-2902.isj20262789Keywords:
Desmoid tumor, FAP, Fibromatosis, GIST, Intra-abdominal fibromatosis, Sporadic desmoid tumorAbstract
Desmoid tumors are rare deep-seated tumors of mesenchymal origin with 2-4 cases per million. Etiology is multifactorial with variable prognosis. These are highly locally invasive but have no ability to metastasize. A 51-year-old male patient who presented with swelling in the right upper abdomen and heaviness in abdomen. On investigating, there was a mass arising from the anti-mesenteric border of the ileum, caecum and ascending colon. Resection of the tumor with the attached ileum, caecum, ascending colon along with the ileo-colic anastomosis was performed. Post operatively, no chemo-radiotherapy was given and patient was on follow-up since then with no recurrence. Desmoid tumor also commonly known as fibromatosis are large soft tissue tumors of mesenchymal origin are locally aggressive tumors with almost no ability to metastasize. Asymptomatic tumors and small tumors can be managed conservatively with close follow-up. Symptomatic and large tumors are usually managed with surgical resection and radiotherapy. Positive margins lead to higher rates of recurrence. This case, reports the rare presentation of a large intra-abdominal sporadic desmoid tumor arising from the anti-mesenteric border of the bowel. Such cases require multi-disciplinary approach with cautious and meticulous resection to prevent capsular rupture.
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