Non-functioning neuroendocrine tumors of the common hepatic duct: a case report and literature review

Maroun Abou-Jaoude; Haydar A. Nasser

doi:10.18203/2349-2902.isj20170869

Authors

Maroun Abou-Jaoude Department of Surgery, The Middle East Institution of Health, Bsalim, Lebanon
Haydar A. Nasser Department of Medical Sciences, Lebanese University, Beirut, Lebanon

DOI:

https://doi.org/10.18203/2349-2902.isj20170869

Keywords:

Extrahepatic biliairy tract, Neuroendocrine tumors

Abstract

Extra-hepatic biliary tree neuroendocrine tumors are not common, accounting for about 0.1 % of all carcinoid tumors. Those affecting the common hepatic duct are very rare and their diagnosis is usually made post-operatively. Poorly differentiated tumors or neuroendocrine carcinomas are commonly seen in elderly, whereas well differentiated tumors, tend to occur in young patients, for whom surgery will lead to good long term results. About 100 cases have been reported in the English medical literature, showing good long term results after surgery for well differentiated (Grades 1 and 2) tumors. Herein, we report a case of an 18-year-old female, complaining from a dull epigastric pain related to a nodule compressing the common hepatic duct. After complete investigation, a laparotomy has been performed and showed a nodular tumor located in the common hepatic duct just above the insertion of the cystic duct with close contact with the pancreatic head distally. En bloc cholecystectomy with bile duct resection was performed and followed by a Roux-en-Y hepatico-jejunostomy. The pathology of the nodule came back to be a neuroendocrine tumor grade 2.

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