Beyond the commons: diagnosis and management of rare intra-abdominal masses-a case series

Indhumathi Nachiyar N.; Arunbabu C.; Dhanaraj P.; Varshini  C.; Gokul Ranjeeth D.

doi:10.18203/2349-2902.isj20252283

Authors

Indhumathi Nachiyar N. Department of General Surgery, Govt. Stanley Medical College, Chennai, Tamil Nadu, India
Arunbabu C. Department of General Surgery, Govt. Stanley Medical College, Chennai, Tamil Nadu, India
Dhanaraj P. Department of General Surgery, Govt. Stanley Medical College, Chennai, Tamil Nadu, India
Varshini C. Department of General Surgery, Govt. Stanley Medical College, Chennai, Tamil Nadu, India
Gokul Ranjeeth D. Department of General Surgery, Govt. Stanley Medical College, Chennai, Tamil Nadu, India

DOI:

https://doi.org/10.18203/2349-2902.isj20252283

Keywords:

Primary small bowel leiomyosarcoma, Primary retroperitoneal melanoma, Ruptured desmoid tumour, Small intestinal lymphoma, Rare intra-abdominal masses, Immunohistochemistry, Multidisciplinary management

Abstract

Rare intra-abdominal masses pose significant challenges in diagnosis and management due to their uncommon presentation and varied etiology. This retrospective case series evaluates four unique cases, including primary retroperitoneal melanoma (PRM), small bowel leiomyosarcoma, ruptured desmoid tumor in familial adenomatous polyposis (FAP), and small intestinal Ewing’s sarcoma. Data were collected from the government Stanley medical college between 2019 and 2023. The study highlights the role of advanced imaging, immunohistochemistry, and multidisciplinary collaboration in improving diagnostic accuracy and treatment outcomes. Prognoses varied, with some cases showing poor outcomes despite aggressive management. This study underscores the necessity of individualized treatment protocols for such rare conditions.

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