Dermatofibrosarcoma protuberans: case series and literature review at the rivers state university teaching hospital, port Harcourt, Nigeria

Itekena E. Wakama; Rex Friday Ogoronte A. Ijah; Linda U. Iroegbu-Emeruem; Monday N. Nkadam; Ibifuro A.  Green

doi:10.18203/2349-2902.isj20251538

Authors

Itekena E. Wakama Rivers State University (RSU), Port Harcourt, Nigeria; Department of Surgery, Rivers State University Teaching Hospital (RSUTH), Port Harcourt, Nigeria
Rex Friday Ogoronte A. Ijah Rivers State University (RSU), Port Harcourt, Nigeria; Department of Surgery, Rivers State University Teaching Hospital (RSUTH), Port Harcourt, Nigeria https://orcid.org/0000-0002-5296-9476
Linda U. Iroegbu-Emeruem Rivers State University (RSU), Port Harcourt, Nigeria; Department of Neuro-Surgery, Rivers State University Teaching Hospital (RSUTH), Port Harcourt, Nigeria
Monday N. Nkadam Rivers State University (RSU), Port Harcourt, Nigeria; Department of Anaesthesiology, Rivers State University Teaching Hospital (RSUTH), Port Harcourt, Nigeria
Ibifuro A. Green Rivers State University (RSU), Port Harcourt, Nigeria; Department of Surgery, Rivers State University Teaching Hospital (RSUTH), Port Harcourt, Nigeria

DOI:

https://doi.org/10.18203/2349-2902.isj20251538

Keywords:

Case series, Dermatofibrosarcoma protuberans, Literature review, Nigeria, Port Harcourt

Abstract

Dermatofibrosarcoma protuberans, first described by Jean Darier and Marcel Ferrand in 1924, can affect various body regions, including the head and neck, trunk and limbs. This case series aimed to document the occurrence of this rare dermatofibrosarcoma protuberans as seen at the Rivers State University Teaching Hospital and the neighbouring referring private clinics over five years (2019-2024). The clinical case notes of patients with dermatofibrosarcoma protuberans were retrieved and data were collected and analysed for the study. Eight dermatofibrosarcoma protuberans cases were observed in the study period. The average age of the patients was 43.9 years, with five females and three males. Most of the patients presented with large, locally advanced, ulcerated masses. All but one underwent wide local excision with a minimum excision margin of 3 cm, followed by chemotherapy. A few dermatofibrosarcoma protuberans were recorded at our centre within the period under study. Wide local excision and adjuvant chemotherapy were offered and adjuvant radiotherapy was recommended but not done.

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