A histopathological surprise of dermatofibrosarcoma protuberance: a case report and review of the literature

Authors

  • Deep Parkash Talreja Department of General Surgery, Ibra Hospital, Masroon, Ibra, Oman
  • Rani Bai Department Obstetrics and Gynecology, Ibra Hospital, Ibra, Masroon, Oman
  • Ahamed Mohamed Elsayed Department of General Surgery, Ibra Hospital, Masroon, Ibra, Oman
  • Hamed Humayid Al-Amri Department of General Surgery, Ibra Hospital, Masroon, Ibra, Oman
  • Fatma Ali Ramadhan Al Lawati Department of Histopathology, Royal Hospital, Muscat, Oman
  • Simran Parkash Department of General Surgery, Ibra Hospital, Masroon, Ibra, Oman
  • Ayman Ahmad Albatanony Department of General Surgery, Ibra Hospital, Masroon, Ibra, Oman

DOI:

https://doi.org/10.18203/2349-2902.isj20250819

Keywords:

Dermatofibrosarcoma protuberans, DFSP, Soft tissue sarcoma, Toe, Lump, CD34, Pathology

Abstract

Dermatofibrosarcoma protuberans (DFSP) represents around 1% to 6% of all soft tissue malignancies, with an annual incidence rate of 4.2 per million individuals. This tumor is most commonly found in the proximal regions of the limbs (10% to 15%), followed by the trunk (40-50%) and chest/shoulders (30% to 40%). Clinically, DFSP often presents as a gradually growing nodule or plaque, initially asymptomatic, which later enters a phase of rapid growth. While DFSP has a significant likelihood of local recurrence, it rarely metastasizes. Children are more likely to have DFSP in distant locations. A study of 27 cases found that 14.8% of childhood DFSP cases involved the hands and feet. DFSP typically presents in individuals between the ages of 20 and 50 years. In this report, we present a case of a young female patient who was incidentally diagnosed with DFSP on the right hallux, confirmed through histopathological analysis, along with its management.

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Published

2025-03-26

How to Cite

Talreja, D. P., Bai, R., Elsayed, A. M., Al-Amri, H. H., Al Lawati, F. A. R., Parkash, S., & Ahmad Albatanony, A. (2025). A histopathological surprise of dermatofibrosarcoma protuberance: a case report and review of the literature. International Surgery Journal, 12(4), 588–592. https://doi.org/10.18203/2349-2902.isj20250819

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Case Reports