A rare case of fascicular spindle cell sarcoma of neck: a malignant peripheral nerve sheath tumor
DOI:
https://doi.org/10.18203/2349-2902.isj20241753Keywords:
MPNST, Neck swelling Neurofibromatosis type-1, SarcomaAbstract
Malignant peripheral nerve sheath tumor-MPNST is rare type of sarcoma making 5% to 10% of sarcoma cases. It grows in the soft tissue of the body and MPNST is sarcoma of cells of sheath that making coverings of peripheral nerve. It is more common in people with genetic condition called neurofibromatosis type-1. Here we report a case of 14-year-old male with right sided neck swelling in the last 5 years without any inflammatory signs. On radiological investigation benign soft tissue tumor- nerve sheath origin was found. We posted patient for Excision of tumor and we found highly vascular friable mass which is excised completely. On histological examination fascicular spindle cell sarcoma found. On reference to oncologist PET-CT was done suggested of no residual growth or metastasis. There is no recurrence till date in our patient.
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