Situs inversus totalis with esophageal cancer: a case report

Sabireen; Gaurav Patel; Prakash K. Patil; Azad Vala; Aditya Reelkar

doi:10.18203/2349-2902.isj20241154

Authors

Sabireen Department of Surgical Oncology, Bombay Hospital and Institute of Medical Sciences, Mumbai, Maharashtra, India https://orcid.org/0000-0001-5961-8874
Gaurav Patel Department of Surgical Oncology, Bombay Hospital and Institute of Medical Sciences, Mumbai, Maharashtra, India https://orcid.org/0000-0002-8642-0473
Prakash K. Patil Department of Surgical Oncology, Bombay Hospital and Institute of Medical Sciences, Mumbai, Maharashtra, India
Azad Vala Department of Surgical Oncology, Bombay Hospital and Institute of Medical Sciences, Mumbai, Maharashtra, India
Aditya Reelkar Department of Surgical Oncology, Bombay Hospital and Institute of Medical Sciences, Mumbai, Maharashtra, India

DOI:

https://doi.org/10.18203/2349-2902.isj20241154

Keywords:

Situs inversus totalis, Lower esophageal cancer, Adenocarcinoma, Thoracoabdominal approach, Esophagectomy

Abstract

Situs inversus is a rare disorder and its association with esophageal cancer is seldom encountered in clinical practice. Its incidence is 1/8000 to 1/25000 live births. Only 12 cases have been reported in the literature so far. Here, we report a case of esophageal cancer with situs inversus totalis, which was successfully managed by esophago-gastrectomy via a high right thoracoabdominal approach and review the relevant literature. Although the surgery was technically challenging due anatomic reversal of organs, it did not differ from the routine surgery. Moreover, it was observed that with careful recognition of mirror image anatomy preoperatively and during surgery, complications can be avoided.

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