A rare case of adult hepatoblastoma mimicking hepatocellular carcinoma- case report and review of literature

Authors

  • Digvijoy Sharma Department of Surgical Gastroenterology, Nizams Institute of Medical Sciences, Punjagutta, Hyderabad, India
  • Nagari Bheerappa Department of Surgical Gastroenterology, Nizams Institute of Medical Sciences, Punjagutta, Hyderabad, India
  • Venu Madhav Thumma Department of Surgical Gastroenterology, Nizams Institute of Medical Sciences, Punjagutta, Hyderabad, India
  • Suryaramchandra Varma Department of Surgical Gastroenterology, Nizams Institute of Medical Sciences, Punjagutta, Hyderabad, India
  • Kunduru Navakishore Department of Surgical Gastroenterology, Nizams Institute of Medical Sciences, Punjagutta, Hyderabad, India
  • Jagan Mohan Reddy Department of Surgical Gastroenterology, Nizams Institute of Medical Sciences, Punjagutta, Hyderabad, India

DOI:

https://doi.org/10.18203/2349-2902.isj20171165

Keywords:

Adult hepatoblastoma, Chemotherapy, Surgical resection

Abstract

Hepatoblastoma (HB) is a rare malignant primary tumour of the liver and occurs mostly in the pediatric group within the first 3 years of life. It is extremely unusual to find hepatoblastoma in adults and is a very rare cause of primary malignant liver tumour in adults and due to this patient may be diagnosed at late stages of the disease at leading to poor prognosis in this group. Reported here a case of a 20-year-old boy with a large liver mass with abdominal pain. Triphasic CT revealed the presence of a large heterogenous tumor in the right lobe of liver suggestive of hepatocellular carcinoma. Patient underwent a right hepatectomy. Final histopathology was reported as Epithelial type hepatoblastoma. The patient had an uneventful post-operative recovery. We present this case for its rarity and ability to masquerade other primary liver tumors in the adult age as seen in our patient.

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Author Biographies

Digvijoy Sharma, Department of Surgical Gastroenterology, Nizams Institute of Medical Sciences, Punjagutta, Hyderabad, India

Senior resident in dept of G.I and HPB surgery, Nizams institute of medical sciences, Punjagutta,Hyderabad-500082

Nagari Bheerappa, Department of Surgical Gastroenterology, Nizams Institute of Medical Sciences, Punjagutta, Hyderabad, India

Professor and Head of Dept of Surgical Gastroenterology, Nizams institute of medical sciences, Punjagutta,Hyderabad-500082

Venu Madhav Thumma, Department of Surgical Gastroenterology, Nizams Institute of Medical Sciences, Punjagutta, Hyderabad, India

Associate professor,Dept of Surgical Gastroenterology, Nizams institute of medical sciences, Punjagutta,Hyderabad-500082

Suryaramchandra Varma, Department of Surgical Gastroenterology, Nizams Institute of Medical Sciences, Punjagutta, Hyderabad, India

Assistant professor,Dept of Surgical Gastroenterology, Nizams institute of medical sciences, Punjagutta,Hyderabad-500082

Kunduru Navakishore, Department of Surgical Gastroenterology, Nizams Institute of Medical Sciences, Punjagutta, Hyderabad, India

Assistant professor,Dept of Surgical Gastroenterology, Nizams institute of medical sciences, Punjagutta,Hyderabad-500082

Jagan Mohan Reddy, Department of Surgical Gastroenterology, Nizams Institute of Medical Sciences, Punjagutta, Hyderabad, India

Assistant Professor, Dept of Surgical Gastroenterology, Nizams institute of medical sciences, Punjagutta,Hyderabad-500082

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Published

2017-03-25

How to Cite

Sharma, D., Bheerappa, N., Thumma, V. M., Varma, S., Navakishore, K., & Reddy, J. M. (2017). A rare case of adult hepatoblastoma mimicking hepatocellular carcinoma- case report and review of literature. International Surgery Journal, 4(4), 1478–1480. https://doi.org/10.18203/2349-2902.isj20171165

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Section

Case Reports