Extrahepatic cholestasis arising from congenital biliary cistern adhesion: a case report

Dedy C. Hariyono; Ibnu Sina Ibrohim; Richard Philo

doi:10.18203/2349-2902.isj20240184

Authors

Dedy C. Hariyono Department of Surgery, Sebelas Maret University, Surakarta, Indonesia
Ibnu Sina Ibrohim Pediatric Surgery Division, Department of Surgery, Dr. Moewardi General Hospital, Surakarta, Indonesia
Richard Philo Faculty of Medicine, Sebelas Maret University, Surakarta, Indonesia

DOI:

https://doi.org/10.18203/2349-2902.isj20240184

Keywords:

BA, Congenital, Adhesion

Abstract

Biliary atresia (BA) is a progressive fibrotic obstructive condition that affects the biliary system, leads bile flow obstruction and the development of newborn jaundice. It is lethal if not treated, with a survival rate of less than 10% by the age of three. Bowel adhesions are anomalous bands of scar tissue that develop between bowel loops. The incidence rate for these bands remains uncertain. This study presents a 2-month-old infant with a progressive yellow discoloration dan diagnosed as BA. Intra operative colangiography was performed and congenital adhesions in the form of bands were discovered.

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